LIOMIOMA INTESTINAL: A PROPÓSITO DE UN PACIENTE
Nivia Castillo Díaz, María Obdulia Benítez Pérez, Ygnacio Ygualada Correa
Resumen
En 1842, Ancell realizó la primera descripción del cilindroma. En 1859, Billroth acuñó el término cilindroma para referirse a las hojas hialinas que persistían después de la maceración del tejido y que conservaban la forma cilíndrica. El carcinoma adenoideo quístico primario cutáneo es un raro tumor maligno de la piel, que clasifica dentro de los tumores de anejos cutáneos con diferenciación ecrina. Se han informado 70 casos de esta enfermedad en la literatura especializada. Es un tumor que afecta, sobre todo, a adultos maduros (edad media 58 años) y es más frecuente en el sexo femenino. Es un tumor solitario más que múltiple; sin embargo, en la forma con lesiones múltiples es fácil reconocerlo, ya que cubre gran parte de la piel del cuero cabelludo, por lo que se denomina tumor en turbante o síndrome de Ancell-Spiegler.
Palabras clave
carcinoma adenoide quístico, neoplasias cutáneas.
Este artículo está licenciado bajo la licencia
Creative Commons Reconocimiento-NoComercial 4.0 Internacional .
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