CUTIS MARMORATA TELANGIECTÁSICA CONGÉNITA: PRESENTACIÓN DE UN PACIENTE
Orlando Rafael Molina Hernández, Luis Monteagudo de la Guardia
Resumen
Se conoce como cutis marmorata telangiectásica congénita a una malformación vascular benigna infrecuente, caracterizada por la presencia de parches localizados o generalizados, frecuentemente asimétricos, con reticulación, asociada en ocasiones a otras lesiones de la piel, y manchas eritematosas o violáceas presentes al nacimiento o de forma temprana.
Se describió, por primera vez, por el pediatra Von Lohuizen en 1922, en Holanda, y desde entonces se han informado alrededor de 100 casos en el mundo. En el año 1970, Petrozzi presentó el primer paciente en los Estados Unidos.
Este artículo está licenciado bajo la licencia
Creative Commons Reconocimiento-NoComercial 4.0 Internacional .
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