ENFERMEDAD DE CAROLI: PRESENTACIÓN DE UN CASO

Lic. Tamara Baldomir Mesa, Dr. Rafael Castillo García, Dra. María Vergara Hidalgo

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La enfermedad de Caroli es una malformación congénita poco frecuente, que se caracteriza por múltiples dilataciones saculares del árbol biliar intrahepático, y fue descrita por Jacques Caroli en 19581. Ocasionalmente afecta también la vía biliar extrahepática, y es por ello que algunos autores –especialmente de países orientales, donde la enfermedad es más frecuente– incluyen la  enfermedad de Caroli en las alteraciones quísticas de la vía biliar2,3.


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