ICTIOSIS LAMELAR. PRESENTACIÓN DE UN PACIENTE
Luis Monteagudo de la Guardia, Nancy Alemán Pedraja, Maribel Navarro Ruiz
Resumen
Los trastornos de la queratinización, también denominados ictiosis, constituyen un grupo importante de trastornos hereditarios, que se caracterizan clÃnicamente por patrones de formación de escamas e histopatológicamente por una hiperqueratosis. Generalmente pueden diferenciarse por los patrones de transmisión hereditaria, las manifestaciones clÃnicas, los defectos asociados y las alteraciones histopatológicas que presentan.
Este artÃculo está licenciado bajo la licencia
Creative Commons Reconocimiento-NoComercial 4.0 Internacional .
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